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Multiple cavernous hemangiomas in the orbit: A case report and review of the literature.

眼眶多发性海绵状血管瘤1例报告并文献复习。

  • 影响因子:1.95
  • DOI:10.1097/MD.0000000000020670
  • 作者列表:"Deng C","Hu W
  • 发表时间:2020-07-17
Abstract

RATIONAL:Cavernous hemangiomas are one of the most common benign primary orbital lesions. These tumors are insidious in onset, slowly progressive and present more often in middle aged women. Multiple orbital cavernous hemangiomas are extremely rare, and only a few cases have been reported in the published literature. PATIENT CONCERNS:Here, we report the diagnosis and treatment of multiple cavernous hemangiomas in the right orbit of a female patient with impaired visual acuity and proptosis of the eye for more than 10 years. DIAGNOSIS:Magnetic resonance imaging of the orbit showed a giant and irregular soft mass filling the intraconal and extraconal space of the right orbit, compressing the right optic nerve. After tumor resection, histopathological examination confirmed the diagnosis of cavernous hemangioma. INTERVENTIONS:A lateral orbitotomy was performed and a total of 13 tumors were excised, with the largest tumor measuring approximately 2.5 × 3.0 cm. OUTCOMES:The visual acuity of the patient was preserved, with only a slightly dilated pupil of the right eye. The follow-up period was 6 months with no signs of recurrence. LESSONS:Multiple cavernous hemangiomas in the orbit is rare and should be excised surgically as soon as possible.

摘要

理性: 海绵状血管瘤是眼眶最常见的良性原发病变之一。这些肿瘤起病隐匿,进展缓慢,多见于中年妇女。多发性眼眶海绵状血管瘤极为罕见,在已发表的文献中仅有少数病例报道。 患者关注的问题: 在这里,我们报告的诊断和治疗的多发性海绵状血管瘤在右侧眼眶的女性患者视力受损和眼球突出超过10年。 诊断: 眼眶磁共振成像显示一个巨大而不规则的软质肿块充满右侧眼眶的内间隙和外间隙,压迫右侧视神经。肿瘤切除后,组织病理检查确诊为海绵状血管瘤。 干预措施: 行外侧眶切开术,共切除肿瘤13个,最大肿瘤约2.5 × 3.0 cm。 结果: 患者的视力得以保留,仅右眼的瞳孔轻微扩张。随访6个月,无复发征象。 教训: 眼眶内多发海绵状血管瘤少见,应尽早手术切除。

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发表时间:2020-01-01
来源期刊:Congenital anomalies
DOI:10.1111/cga.12331
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影响因子:2.36
发表时间:2020-01-01
来源期刊:Platelets
DOI:10.1080/09537104.2019.1581922
作者列表:["Szanto T","Nummi V","Jouppila A","Brinkman HJM","Lassila R"]

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DOI:10.1177/1078155219843987
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